Associated Papers
Rescue of Rare CFTR Trafficking Mutants Highlights a Structural Location-Dependent Pattern for Correction.
Zacarias S et al.
International Journal of Molecular Sciences, 2023
36834620 (PubMed )
Supplement: ijms-24-03211-s001.zip › ijms-2071953-supplementary.pdf
Impact of cholesterol and Lumacaftor on the folding of CFTR helical hairpins.
Schenkel M et al.
Biochimica Et Biophysica Acta. Biomembranes, 2023
CFTR transmembrane segments are impaired in their conformational adaptability by a pathogenic loop mutation and dynamically stabilized by Lumacaftor.
Krainer G et al.
The Journal of Biological Chemistry, 2020
Structural effects of extracellular loop mutations in CFTR helical hairpins.
Chang YH et al.
Biochimica Et Biophysica Acta. Biomembranes, 2018
Misfolding of the cystic fibrosis transmembrane conductance regulator and disease.
Cheung JC et al.
Biochemistry, 2008
Role of the extracellular loop in the folding of a CFTR transmembrane helical hairpin.
Wehbi H et al.
Biochemistry, 2007
A combined analysis of the cystic fibrosis transmembrane conductance regulator: implications for structure and disease models.
Chen JM et al.
Molecular Biology and Evolution, 2001
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