Associated Papers
Changes in sputum viscoelastic properties and airway inflammation in primary ciliary dyskinesia are comparable to cystic fibrosis on elexacaftor/tezacaftor/ivacaftor therapy.
Nussstein H et al.
The European Respiratory Journal, 2026
People with cystic fibrosis with high sputum neutrophil elastase on elexacaftor-tezacaftor-ivacaftor exhibit worse pulmonary function and pro-inflammatory airway milieu.
Cammarata-Mouchtouris A et al.
Scientific Reports, 2025
Restoring chloride efflux in cystic fibrosis with TMEM16a antisense oligonucleotides.
Mitri C et al.
Molecular Therapy : the Journal of the American Society of Gene Therapy, 2025
Alpha-1 antitrypsin deficiency: genetics, clinical manifestations, AI prognostics, and advanced imaging in liver disease.
Rajab I et al.
Annals of Medicine and Surgery (2012), 2025
Mechanisms of Lung Cancer Development in Cystic Fibrosis Patients: The Role of Inflammation, Oxidative Stress, and Lung Microbiome Dysbiosis.
Pagliaro R et al.
Biomolecules, 2025
Laboratory Tools to Predict CFTR Modulator Therapy Effectiveness and to Monitor Disease Severity in Cystic Fibrosis.
Bacalhau M et al.
Journal of Personalized Medicine, 2024
Proteomic profiling of sweat in patients with cystic fibrosis provides new insights into epidermal homoeostasis.
Cornet M et al.
Skin Health and Disease, 2023
Impact of CFTR Modulators on the Impaired Function of Phagocytes in Cystic Fibrosis Lung Disease.
Meoli A et al.
International Journal of Molecular Sciences, 2022
Neutrophil dysfunction in cystic fibrosis.
Yonker LM et al.
Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society, 2021
Increased Inflammatory Markers Detected in Nasal Lavage Correlate with Paranasal Sinus Abnormalities at MRI in Adolescent Patients with Cystic Fibrosis.
Chung J et al.
Antioxidants (basel, Switzerland), 2021
VJ Segment Usage of TCR-Beta Repertoire in Monozygotic Cystic Fibrosis Twins.
Fischer S et al.
Frontiers in Immunology, 2021
Single-Cell Transcriptional Archetypes of Airway Inflammation in Cystic Fibrosis.
Schupp JC et al.
American Journal of Respiratory and Critical Care Medicine, 2020
Myeloperoxidase oxidation of methionine associates with early cystic fibrosis lung disease.
Chandler JD et al.
The European Respiratory Journal, 2018
Treatment with rhDNase in patients with cystic fibrosis alters in-vitro CHIT-1 activity of isolated leucocytes.
Weckmann M et al.
Clinical and Experimental Immunology, 2016
A novel lipidomic strategy reveals plasma phospholipid signatures associated with respiratory disease severity in cystic fibrosis patients.
Guerrera IC et al.
Plos One, 2009
Cystic fibrosis chronic rhinosinusitis: a comprehensive review.
Chaaban MR et al.
American Journal of Rhinology & Allergy, 0