Associated Papers
Drosophila melanogaster as a model to study autophagy in neurodegenerative diseases induced by proteinopathies.
Santarelli S et al.
Frontiers in Neuroscience, 2023
Variation in the vulnerability of mice expressing human superoxide dismutase 1 to prion-like seeding: a study of the influence of primary amino acid sequence.
Ayers JI et al.
Acta Neuropathologica Communications, 2021
Distinct conformers of transmissible misfolded SOD1 distinguish human SOD1-FALS from other forms of familial and sporadic ALS.
Ayers JI et al.
Acta Neuropathologica, 2016
Neuron-specific expression of mutant superoxide dismutase is sufficient to induce amyotrophic lateral sclerosis in transgenic mice.
Jaarsma D et al.
The Journal of Neuroscience : the Official Journal of the Society for Neuroscience, 2008
How do ALS-associated mutations in superoxide dismutase 1 promote aggregation of the protein?
Shaw BF et al.
Trends in Biochemical Sciences, 2007
Superoxide dismutase-1 mutation-related neurotoxicity in familial amyotrophic lateral sclerosis.
Shibata N et al.
Amyotrophic Lateral Sclerosis and Other Motor Neuron Disorders : Official Publication of the World Federation of Neurology, Research Group on Motor Neuron Diseases, 2000
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