Associated Papers
Overexpression of bank vole PrP(I109) in mice induces a spontaneous atypical prion disease with sex-dependent onset, early NfL elevation, and universal prion strain permissiveness.
Eraña H et al.
Acta Neuropathologica Communications, 2026
Substitution of histidine 95 by tyrosine in the prion protein causes spontaneous neurodegeneration in transgenic mice.
Torres JM et al.
Plos Pathogens, 2025
Infecting human brain organoids with FFI or sCJD preserves prion traits regardless of host genotype.
Groveman BR et al.
Npj Dementia, 2025
Altered energy metabolism in Fatal Familial Insomnia cerebral organoids is associated with astrogliosis and neuronal dysfunction.
Foliaki ST et al.
Plos Genetics, 2023
Pathogenic Prion Protein Isoforms Are Not Present in Cerebral Organoids Generated from Asymptomatic Donors Carrying the E200K Mutation Associated with Familial Prion Disease.
Foliaki ST et al.
Pathogens (basel, Switzerland), 2020
Genetic Factors in Mammalian Prion Diseases.
Mead S et al.
Annual Review of Genetics, 2019
Pressure Reveals Unique Conformational Features in Prion Protein Fibril Diversity.
Torrent J et al.
Scientific Reports, 2019
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